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City Oxford / Lachenbruch / Baltimore / TNF / / Company Goldman / Juvenile Dermatomyositis Research Group / Clinical Studies Group / LG / Lehman / Juvenile Dermatomyositis Disease Activity Collaborative Study Group / Pilkington / / Country Brazil / Canada / United Kingdom / Ireland / / / Event Product Recall / Product Issues / / Facility Cellular Immunology Laboratory / Laboratory of Medical Investigation / American College of Rheumatology / National Institute of Arthritis / / / IndustryTerm damage tools / Physical function assessment tools / treatment of the disease / / MedicalCondition inflammatory response / non-erosive arthritis / juvenile idiopathic inflammatory myopathies / childhood inflammatory myopathies / JE / myopathy / perivascular inflammatory exudate / INTRODUCTION Juvenile dermatomyositis / acquired lipodystrophy / facial erythema / hepatitis B / flexion contractures / clinical manifestations Dysphagia / review article Juvenile dermatomyositis / D Muscle biopsy showing necrosis / cutaneous dermatomyositis / chronic inflammation / T lymphocyte CD8+-mediated inflammation / symmetrical proximal muscle weakness / Prognosis Juvenile dermatomyositis / inflammatory myositis / Cláudia Goldenstein-Schainberg2 ABSTRACT Juvenile dermatomyositis / hirsutism / juvenile dermatomyositis / Inflammatory Myopathies / illness / severe disease / idiopathic inflammatory myopathies / severe and prolonged disease / calcinosis / lipodystrophy / inflammatory myopathy / vasculitis / autoimmune myositis / Heliotrope rash / untreated disease / dysphagia / rheumatic diseases / fever / active disease / muscle disease / infection / chronic aspiration / validated disease / baseline disease / inflammatory / monocyclic disease / CONCLUSION Juvenile dermatomyositis / glucose intolerance / refractory juvenile dermatomyositis / juvenile systemic lupus erythematosus / esophageal dysmotility / TB / Untreated Juvenile Dermatomyositis / inflammatory process / dysphonia and severe pulmonary involvement / osteopenia and even established osteoporosis / true vasculitis / Tenosynovitis / muscle weakness / Infectious / muscle diseases / persistent disease / symmetrical muscle weakness / Arthralgias / violet erythema / fatigue / Juvenile Idiopathic Inflammatory Myopathy / greater bone resorption / Cutaneous manifestations Erythema / Cossermelli W. Pericardial tamponade / MS / myocarditis / primary pulmonary involvement / Pericarditis / inflammatory activity / insulin resistance / necrosis / early juvenile dermatomyositis / cutaneous erythema / disease / typhoid fever / idiopathic inflammatory myopathy / Global disease / adult disease / hypopigmentation / adult inflammatory myopathies / dysphonia / tumor necrosis / acanthosis nigricans / violaceous erythema / diabetes mellitus / autoimmune disease / cholera / clinically amyopathic dermatomyositis / inflammation / thrombosis / juvenile-onset dermatomyositis / infectious disease history preceding juvenile dermatomyositis / dermatomyositis / Polymyositis / / MedicalTreatment physical therapy / intravenous therapy / immunosuppressive therapy / / NaturalFeature Apaz MT / / Organization Rheumatology Department / Hospital for Sick Children in Toronto / Medical School / European League Against Rheumatism Disease Activity Core Set for the Evaluation of Response / American College of Rheumatology / National Institute of Arthritis and Musculoskeletal / Provisional Paediatric Rheumatology International Trials Organization / Laboratory of Medical Investigation / Pediatric Rheumatology International Trials Organization / Pediatric Rheumatology International Trials Organisation / / Person Bohan / Oliveira Sato / Arnaldo / Arch Pathol / Peter Diagnostic / Gene Polymorphisms / Cláudia Goldenstein-Schainberg / / / Position Prime Minister / physician / Assisting Physician / Ferriani VP / VP / Roscoe / Professor of FMUSP / Chief / / Product methylprednisolone / cyclosporine / Prednisolone / prednisone / azathioprine / GC / cyclophosphamide / testosterone / / ProvinceOrState South Dakota / / RadioStation Huber AM / North Am 2005 / Am 2002 / Am 2007 / Sallum AM / Reed AM / / Technology X-ray / apoptosis / gene expression / CAT / alpha / Av / polymerization / MRI / / SocialTag