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Channelopathy / Cystic fibrosis / Pediatrics / Myeloperoxidase / Lactoperoxidase / Hypothiocyanite / Mucus / Acute respiratory distress syndrome / Health / Medicine / Biology


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City

Philadelphia / /

Company

Sigma-Aldrich / GE / Invitrogen Inc. / /

Country

United States / /

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Event

Product Issues / /

Facility

Howard Hughes Medical Institute / Osaka University / University of Pennsylvania Medical Center / University of Pennsylvania / /

IndustryTerm

macrophage product / therapy for CF disease / therapy for CF lung disease / predominant site / respiratory and digestive systems / therapy for cystic fibrosis / chemical reduction / phosphate buffer solution / digestive and respiratory systems / /

MedicalCondition

inflammatory enzyme myeloperoxidase / MPO-produced injuries / progressive / destructive intraluminal inflammation / ystic fibrosis / Lower airway inflammation / cases inflammation / chronic irritation / HAE / chronic insidious injuries / Airway inflammation / CF lung illness / Pulmonary / excessive inflammation / slow disease / subtotal myeloperoxidase deficiency / Lung injuries / pulmonary inflammation / severe lung injuries / severe injuries / cystic fibrosis / MPO-caused cell injuries / cardiovascular diseases / inflammatory diseases / clinical infection / lung cancers / mouse neuroblastoma cell line / asthma / coronary artery stenosis / common fatal hereditary disease / atherosclerosis / cystic fibrosis lung disease / CF disease / MPO-caused injuries / severe cell injuries / peripheral insulin resistance / diabetes / cardiovascular disease / CF-lung illness / congenital MPO deficiency / certain cancers / Primary inflammation / lung cancer / Pulmonary dysfunction / lung illness / Diabetes mellitus / Parkinson’s disease / diseases / lung infection / pleiotropic disease / coronary artery disease / previously reported lung cell injuries / infection / airway disease / beta-cell dysfunction / thrombus / neurodegenerative diseases / deficiency / inflammation / CF lung disease / bactericidal and inflammatory agents / H2O2-caused injuries / inflammatory / injuries / /

NaturalFeature

Ashby MT / /

Organization

University of Pennsylvania / University of Pennsylvania Medical Center / Osaka University / Zhe Lu1 Department of Physiology / Cystic Fibrosis Foundation / Howard Hughes Medical Institute / /

Person

Van Der Vliet / Yanping Xu / T. Hoshi / /

Position

investigator / appreciated mediator / reactive Author / Quinton PM / /

Product

balanced salt / Ibuprofen / M-16 / OCl / CFTR / CFTR channels / CFTR gene / protection / /

ProvinceOrState

Pennsylvania / /

Technology

Cloning / apoptosis / drug development / /

URL

www.pnas.org͞cgi͞doi͞10.1073͞pnas.0911412106 / /

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