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City Boston / / Company Eaton / Ó 2013 Elsevier Inc. / / Country United States / / / Facility Spaulding Rehabilitation Hospital / Women’s Hospital / / IndustryTerm important tool / appropriate biopsy site / / MedicalCondition certain myopathies / Multicore/minicore myopathy / distal muscle weakness / radiculopathy / muscular dystrophy / McArdle disease / statin myopathies / carbohydrate metabolism causing muscle weakness / HIV / Centronuclear/myotubular myopathy / active myositis / myopathy / Trichinosis / Steroid myopathy / connective and fatty tissue / chronic myopathies / entrapment neuropathy / neurogenic and neuromuscular junction disorders / neuromuscular junction disorders / dysfunction / inherited myopathies / electrical myotonia / severe chronic myopathies / presynaptic neuromuscular junction disorder / Pompe Disease Pompe disease / hereditary inclusion body myopathies / suspected myopathies / Lipid storage myopathies / Critical illness myopathy / polyneuropathy / best-known muscular dystrophies / motor neuron disorders / hereditary / progressive muscle disorders / chronic nature / contracture / toxic myopathy / acid alpha-glucosidase deficiency / critical illness / muscle contraction / end-stage muscular dystrophies / inflammatory changes / toxic myopathies / muscle disorder / demyelination / selected muscle diseases / Myotonia congenita / selected infectious agents / Inflammatory myopathies / certain glycogen storage disorders / myotonias / long-standing disease / Central core myopathy / idiopathic inflammatory myopathies / presynaptic neuromuscular junction transmission disorders / motor neuron disease / proximal muscle weakness / Pompe disease / myopathies / Toxic/necrotic myopathies / myopathic disorders / Lambert-Eaton myasthenic syndrome / enzyme deficiency / critical illness polyneuropathy / mild axonal sensory polyneuropathy / Myotonic disorders / necrosis / Congenital myopathies / periodic paralysis / disease / potassium-sensitive periodic paralysis / selected myopathies / unrelated chronic neurogenic changes / dyspnea / distal muscular dystrophies/myopathies / suspected myopathy / metabolic myopathy / Nemaline rod myopathy / Cholesterol-lowering agent myopathies / Myotonic dystrophy / chronic steroid administration / idiopathic inflammatory myopathy / chronic end-stage myopathies / clinical myotonia / Metabolic myopathies / Toxic/Necrotic Myopathies Toxic/necrotic myopathies / myotonic disorder / concomitant polyneuropathy / congenital and metabolic disorders / primary muscle disease / several other myopathies / mitochondrial myopathies / myositis / Toxoplasmosis / muscle disease / chronic neurogenic process / Muscular dystrophies / specific disease / deficiency / degenerative spine disease / myofibrillar myopathies / inflammation / Inclusion Body Myositis IBM / Immune-mediated necrotizing myopathy / body myositis / dermatomyositis / debrancher enzyme deficiency / inflammatory / Polymyositis/Dermatomyositis Polymyositis / Polymyositis / paramyotonia congenita / / MedicalTreatment immunosuppressive therapies / / Organization Harvard Medical School / Women’s Hospital / Spaulding Rehabilitation Hospital / Medical Research Council / Department of Neurology / Brigham and Women / Department of Physical Medicine and Rehabilitation / / Person Sabrina Paganoni / Anthony Amato / / Position Corresponding author / / ProvinceOrState Massachusetts / / RadioStation Clin N Am 24 / / Technology alpha / diagnostic tests / 3 Suggested EDX protocol / / URL http / SocialTag