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1136 REVIEW Primary ciliary dyskinesia: current state of the art Andrew Bush, Rahul Chodhari, Nicola Collins, Fiona Copeland, Pippa Hall, Jonny Harcourt,
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City

Leicester / Southampton / London / /

Company

National Commissioning Group / UK Cystic Fibrosis Nurse Specialist Group / Halbert SA / Proc Natl Acad Sci U S A / DNAH7 / CF Trust / /

Country

United Kingdom / /

Currency

pence / /

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Event

FDA Phase / Product Issues / /

Facility

N N N N N N Complex / Royal Brompton Hospital / Charing Cross Hospital / Arch Dis Child / Great Ormond Street Hospital / Leeds Metropolitan University / Pippa Hall / Leicester Royal Infirmary / Westminster Hospital / University of Leicester / UCL Institute of Child / /

IndustryTerm

proper diagnostic services / secretory otitis media / diagnostic services / otitis media / recurrent acute otitis media / Online First / axonemal heavy chain / dynein heavy chain / positive expiratory pressure devices / /

MedicalCondition

inflammatory response / suppurative lung diseases / chronic upper / hydrocephalus / Cilia-related diseases / secretory otitis media / retinitis pigmentosa / liver and kidney disease / neonatal pneumonia / likely primary ciliary dyskinesia / dysfunction / nasal polyps / airway inflammation / REVIEW Primary ciliary dyskinesia / Haemophilus influenza / primary ciliary dyskinesia presenting / Usher syndrome / multisystem disease / primary ciliary dyskinesia syndrome / ciliary disorientation / O’Callaghan C. Primary ciliary dyskinesia / Male infertility / otitis media / N Chronic / asthma / Infertility / either hearing loss / Radhakrishna U. Primary ciliary dyskinesia / Kartagener syndrome / wet-sounding cough / secondary ciliary dysfunction / X-linked retinitis / influenza A / ciliary dyskinesia courses / given asthma / oesophageal disease / infection / Situs inversus / respiratory infection / chronic infection / chronic ill health / disorders / abnormal movement / autosomal recessive disease / ciliary dyskinesia / Pseudomonas / upper and lower airways infections / otitis / Central microtubular agenesis causing primary ciliary dyskinesia / recurrent acute otitis media / recurrent infections / childhood Ectopic pregnancy / Primary ciliary dyskinesia / Witt M. Primary ciliary dyskinesia / heart disease / rhinitis / chronic mucus pooling / renal disease / Isolated dry cough / speech delay / autosomal recessive disorder / sinusitis / chronic airway inflammation / cystic fibrosis / chronic sinusitis / upper and lower respiratory tract infection / hearing loss / Medical interventions PCD lung disease / Dyer J. Cystic fibrosis / Kartagener’s syndrome / N Respiratory distress / laterality19 Polycystic kidney / non-cystic fibrosis bronchiectasis / Siewert’s/Kartagener’s syndrome / disease / lower respiratory tract infection / human genetic disorders / X linked retinitis pigmentosa syndrome / milder hearing loss / Polycystic kidney disease / biliary atresia / retinal degeneration / Chronic mucoid rhinorrhoea / chronic lung disease / minor epistaxis / bronchiectasis / cough / inflammation / older children severe sinusitis / respiratory disease / retinitis / Cilia dysfunction / upper and lower airway disease / /

MedicalTreatment

speech therapy / Lobectomy / antibiotics / intravenous therapy / physiotherapy / counselling / sinus surgery / intracytoplasmic sperm injection / /

Organization

University of Leicester / Leeds Metropolitan University / Leeds / Charing Cross Hospital / UCL Institute of Child / Department of Paediatric Respiratory Medicine / NHS / Royal Brompton Hospital / Great Ormond Street Hospital / Faculty of Health / Westminster Hospital / Adolescent Paediatric Unit / /

Person

Nicola Collins / Hannah M Mitchison / Arch Dis / Claire Hogg / Gill Phillips / Jane Lucas / Rahul Chodhari / Andrew Bush / Mohamed Hariri / Prasad A. Physiotherapy / /

Position

General / paediatric nurse specialist / surgeon / Usher / respiratory nurse / nurse / care and counselling.42 The nurse specialist / nurse specialist / /

Product

triad / ciprofloxacin / Flutter36 / lung function / PCD / /

Technology

Genomics / adc / tomography / ultrasound / transplantation / /

URL

www.archdischild.com / /

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