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City Pavia / / Company Hunt SA / Proc Natl Acad Sci U S A / Goldman / Buxton AE / Molecular Cardiology Laboratories / Sumitomo / Donaldson / / Country Italy / Israel / / / Facility University of Pavia / American College of Cardiology/American Heart Association Task Force / / IndustryTerm knock-in mouse model carrier / / MedicalCondition ventricular tachycardia / nonsustained supraventricular tachycardia / Bidirectional tachycardia / both chronic treatment / catecholaminergic polymorphic ventricular tachycardia / bidirectional ventricular tachycardia / mendelian diseases / autosomal recessive catecholamine-induced polymorphic ventricular tachycardia / distinct periodic paralysis / AndersenTawil syndrome / inherited arrhythmogenic disorders / Coumel P. Catecholaminergic polymorphic ventricular tachycardia / chronic therapy / Andersen’s syndrome / Syncope / Isolated atrial ectopic beats / catecholaminergic polymorphic ventricular tachycardia genetic testing / skeletal muscle disorders / bradycardia / tachycardia / idiopathic ventricular fibrillation / severe disorder / inherited arrhythmogenic diseases / cardiac arrest / Overvad H. Intermittent muscular weakness / exercise-/emotion-induced syncopal episodes / inherited arrhythmogenic disorder / extrasystoles / lethal disorder / periodic paralysis / disease / sudden cardiac death / catecholaminergic polymorphic ventricular tachycardia using / Andersen-Tawil syndrome / familial cardiac arrhythmia / diagnosis Syncope / unexplained cardiac arrest / juvenile sudden cardiac death / Niimura I. Catecholaminergic polymorphic ventricular tachycardia / neurologic disorders / polymorphic ventricular tachycardia / Supraventricular arrhythmia / ventricular fibrillation / Supraventricular tachycardia / exercise-/emotion-triggered syncope / atrial fibrillation / KEYWORDS Arrhythmia / syncopal episodes / KCNJ2 AndersenTawil syndrome / Tawil R. Andersen’s syndrome / Adams-Stokes syndrome / syndrome / / Organization University of Pavia / European Society / Heart Rhythm Society / Cardiology/American Heart Association Task Force / Cardiology Committee for Practice Guidelines / the American College / European Heart Rhythm Association / / Person Ann Neurol / Silvia G. Priori / Cruz Filho / Mayo Clin / Ben Asher / Carlo Napolitano / / Position Walker / physician / / Product Metra / nadolol / / ProvinceOrState Vermont / New Mexico / / Technology human genome / / SocialTag