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Posttranslational modification / Filaggrin / Stratum corneum / Keratinocyte / Protease / Corneocyte / Serpin / Serine protease / Claudin / Biology / Cell biology / Proteins


JCB: ARTICLE The epidermal barrier function is dependent on the serine protease CAP1/Prss8 Céline Leyvraz,1 Roch-Philippe Charles,1 Isabelle Rubera,1 Marjorie Guitard,1 Samuel Rotman,2 Bernadette Breiden,3 Konrad Sandh
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City

LEYVRAZ ET / Claudin / Lausanne / Charlestown / Illkirch / /

Company

Carl Zeiss MicroImaging Inc. / IgG / Rockefeller University Press / Zymed Laboratories / Nikon / QIAGEN / Merck / Progen Biotechnik GmbH / GE Healthcare / Covance / Pierce Chemical Co. / Cre / Jackson ImmunoResearch Laboratories / /

Country

Germany / Switzerland / Poland / France / Japan / United States / /

Currency

USD / /

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Event

Product Issues / /

Facility

Kyoto University / Cutaneous Biology Research Center / TJ complex / COOH terminus / /

IndustryTerm

profilaggrin processing / protein processing / inappropriate processing / defective filaggrin processing / proposed consensus site / control / proteolytic processing / filaggrin processing / filaggrin processing pattern / cellular imaging / knockout / profilaggrin-derived proteolytic products / polybasic cleavage site / /

MedicalCondition

Harlequin ichthyosis / hormone-refractory human prostate cancers / ovarian cancers / CAP1/ Prss8 deficiency / atopic dermatitis / skin disorders / paroxysmal nocturnal hemoglobinuria / alopecia / methanol dehydration / harlequin disease / pulmonary edema / disorder / CAP1/Prss8 deficiency / severe dehydration / cancer / disease / skin abnormalities / rapid / fatal dehydration / Increased dehydration / PFA / epidermal deficiency / deficiency / ichthyosis / rapid and fatal dehydration / congenital ichthyosis / genetic disorders / dehydration / /

MedicalTreatment

rehydration / /

NaturalFeature

Na channel / /

Organization

Harvard / Switzerland Kekulé-Institut für Organische Chemie / Institut de Genetique / Universität Bonn / Cutaneous Biology Research Center / US Federal Reserve / Rockefeller University / Swiss National Science Foundation / Kyoto University / Kyoto / /

Person

Dale / Friedrich Beermann / Hans-Peter Gaeggeler / Yannis Krempp / Q. Tong / Jean-Daniel Horisberger / Nat / Sakura Finetek / Daniel Metzger / Nicole Fowler-Jaeger / J. Physiol / Pierre Chambon / K.L. Harkleroad / Bernard Rossier / Céline Leyvraz / Pearton / J.P. Johnson / Kam / Miguel van Bemmelen / Bettina Kircharz / Edith Hummler / Jean-Yves Chatton / Anne-Marie Mérillat / J. Van Vlijmen-Willems / W. Nirunsuksiri / /

Position

model for pulmonary edema / RT / General / D.J. / Representative / /

Product

triad / SC / early neonatal death / profilaggrin / stratum corneum / epidermal barrier function / paroxysmal nocturnal hemoglobinuria / GPI-anchored proteins / mice / epidermis / glycosyl phosphatidylinositol anchor synthesis / filaggrin processing / epidermal lipid matrix composition Components / /

ProvinceOrState

British Columbia / South Carolina / Massachusetts / /

Technology

alpha / antibodies / ultrasound / genotyping / digital camera / laser / gene targeting / Genotype / recombination / /

URL

http /

SocialTag