Pyruvate decarboxylase

Results: 2



#Item
1Autoantigens / Pediatrics / Branched-chain amino acids / Maple syrup urine disease / Branched-chain alpha-keto acid dehydrogenase complex / Newborn screening / Dihydrolipoamide dehydrogenase / Pyruvate dehydrogenase / Inborn error of metabolism / Health / Rare diseases / Medicine

Disease Name MAPLE SYRUP URINE DISEASE (MSUD) (BRANCHED-CHAIN KETOACIDURIA; BRANCHED-CHAIN ALPHA-KETO ACID DEHYDROGENASE DEFICIENCY; MSUD; KETO ACID DECARBOXYLASE DEFICIENCY) Organic aciduria Classification:

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Source URL: www.idph.state.ia.us

Language: English - Date: 2007-06-25 16:37:11
2Metabolism / Cellular respiration / Pyruvate decarboxylase / Pyruvate dehydrogenase complex / Hydroxypyruvate decarboxylase / Pyruvate dehydrogenase / Enzyme inhibitor / Pyruvate decarboxylation / Carboxy-lyases / Chemistry / Biology / Biochemistry

305 Biochem. J[removed], [removed]Printed in Great Britain) Inactivation of pyruvate decarboxylase by 3-hydroxypyruvate Greg THOMAS, Russell DIEFENBACH and Ronald G. DUGGLEBY*

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Source URL: rdbiotech.drivehq.com

Language: English - Date: 2007-08-19 19:46:17
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